Why does my baby pee smell like maple syrup?

Babies with MSUD are unable to break down amino acids called leucine, isoleucine and valine. Very high levels of these amino acids are harmful. One of the characteristic symptoms of MSUD is sweet-smelling urine, which gives the condition its name.

Why does my baby smell like pancake syrup?

Symptoms of classic MSUD appear in newborns within 48 hours of birth. In older children, signs of intermediate, intermittent, and thiamine-responsive MSUD usually develop before age seven. All four types of MSUD have symptoms including: Urine, sweat, or earwax that smells like maple syrup or burnt sugar.

Can babies have maple syrup urine disease?

Maple syrup urine disease (MSUD) is a rare metabolic disorder that some babies are born with. It’s caused by a defect in the enzymes that break down some amino acids. Most newborn babies in the United States have their blood tested for MSUD as part of newborn screening.

Is maple syrup urine disease fatal?

The condition gets its name from the distinctive sweet odor of affected infants’ urine. It is also characterized by poor feeding, vomiting, lack of energy (lethargy), abnormal movements, and delayed development. If untreated, maple syrup urine disease can lead to seizures, coma, and death.

IT IS SURPRISING:  How much can you carry when pregnant?

What causes a maple syrup smell?

Fenugreek contains an extremely potent aromatic compound called solotone. Also present in lovage, some aged rums, and molasses, solotone passes through the body, and when consumed in heavy amounts, can prompt a sweet maple-y odor in sweat and urine.

What is a maple baby?

Babies with MSUD are unable to break down amino acids called leucine, isoleucine and valine. Very high levels of these amino acids are harmful. One of the characteristic symptoms of MSUD is sweet-smelling urine, which gives the condition its name.

What can cause sweet-smelling urine?

5 causes of sweet-smelling urine

  • UTI. Urinary tract infections (UTIs) are very common infections of the urinary system. …
  • Hyperglycemia and diabetes. Hyperglycemia occurs when you have abnormally high blood sugar levels. …
  • Diabetic ketoacidosis. …
  • Foetor hepaticus. …
  • Maple syrup urine disease.

Why does my babies pee smell sweet?

Conditions Maple Syrup Urine Disease. Maple syrup urine disease (MSUD) is a condition in which the body is unable to break down certain proteins. The condition is named for the sweet odor of the urine of untreated babies.

How can I tell if my baby has diabetes?

The signs and symptoms of type 1 diabetes in children usually develop quickly, and may include:

  • Increased thirst.
  • Frequent urination, possibly bed-wetting in a toilet-trained child.
  • Extreme hunger.
  • Unintentional weight loss.
  • Fatigue.
  • Irritability or behavior changes.
  • Fruity-smelling breath.

At what age is maple syrup urine disease diagnosed?

The onset and symptoms of intermediate MSUD may be neonatal, but the majority of children are diagnosed between the ages of five months and seven years.

IT IS SURPRISING:  Your question: How do I deep clean before my baby?

What is Hunter syndrome disease?

Hunter syndrome is a very rare, inherited genetic disorder caused by a missing or malfunctioning enzyme. In Hunter syndrome, the body doesn’t have enough of the enzyme iduronate 2-sulfatase.

Should I be worried if my urine smells sweet?

Sweet-smelling urine may be a sign of uncontrolled diabetes or a rare disease of metabolism. Liver disease and certain metabolic disorders may cause musty-smelling urine.

What vitamin makes you smell like maple syrup?

Supplementing fenugreek may cause body secretions, including urine, to smell like maple syrup. This is due to a metabolite called sotolon.